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NUR 201 ( LATEST 2024 / 2025 ) TEST 6 | GUARANTEED A+ ACTUAL QUESTIONS AND ANSWERS
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NUR 201 ( LATEST 2024 / 2025 ) TEST 6 | GUARANTEED A+ ACTUAL QUESTIONS AND ANSWERS
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NUR 201 Test 61. cystic fibrosis (CF)
Answer
hereditary disorder of the exocrine glands characterized by excess mucus production in the
respiratory tract, pancreatic deficiency, and other symptoms
2. Pseudomonas
Answer
Common causes of pneumonia in CF
3. CF most at risk ethnicity is
Answer
caucasians
4. CFTR gene
Answer
a gene that codes for a protein involved in chloride and water transport across membranes. In
patients with cystic fibrosis, a mutation in this gene disrupts chloride and water transport across
membranes.
5. CFTR is an disorder
Answer
autosomal recessive
6. CF pathophysiology
Answer
The CFTR protein promotes chloride transport at the cellular level. Mutations disrupt these
functions to varying degrees.
Major result is the formation of thick sticky mucus in the epithelial cells of the lungs, pancreas,
liver, salivary glands, and testes, causing reduced organ function over time.
,7. Chloride (electrolyte)
Answer
Aids in maintaining a normal balance of bodily fluids
8. CF mucus secretions have too much and too little
Answer
salt, water
9. Pancrelipase (Creon)
Answer
*class*
pancreatic enzyme
*Indication*
pancreatic insufficiency, ductal obstruction
*Action*
replacement of pancreatic enzymes
lipase, amylase, protease
*Nursing Considerations*
- contraindicated with pig products allergy
- can cause shortness of breath, nausea, diarrhea, rash
- assess nutritional status
- monitor for steatorrhea
,- may increase uric acid levels
- instruct patient to follow diet
- take with meals and snacks
10. CF clinical manifestations
Answer
-chronic cough
-sinusitis (nasal polyps)
-meconium ileus (7-10% of newborns)
-pancreatic insufficiency
-rectal prolapse
-frequent respiratory infections
-persistent coughing
-audible wheezing
-dyspnea
-thick sputum
-very foul fatty stools
11. CF testing
Answer
-confirmatory test = sweat chloride test (>60mEq/L is positive for CF)
(gold standard)
12. CF Digestive system
Answer
mucus can block tubes or ducts in pancreas and prevent enzymes from reaching intestines.
infants do not pass meconium. gas, severe constipation, poor weight gain/growth, diarrhea
13. CF reproductive system
Answer
1. delayed puberty in females
2. fertility can be inhibited by highly viscous cervical secretions, which act as a plug and block
, sperm entry
3. males are usually sterile as a result of the blockage of the vas deferens by abnormal
secretions or the failure of the normal development of duct structures
14. CF Nutrition
Answer
-Use age appropriate BMI to assess ht + wt
-pancreatic enzymes w/ meals + snacks
-High pro, kcal, fat, salt
-15-20% pro
-CHO 45-55%
-35-40% fat
- Additional appropriate doses water sol vit/min
- Supp water sol forms fat sol (A,D, E, K)
15. CF medications
Answer
o Bronchodilators
o Antibiotics
o O2 only during acute episodes, maybe at night - because they live with a chronical- ly high CO2
- if they are over oxygenated will give them problems because repressing breathing
16. Kalydeco (ivacaftor)
Answer
first-in-class oral cystic fibrosis medication that treats the G551D-CFTR protein defect
17. Dornase alfa (Pulmozyme)
Answer
decreases viscosity of mucus and improves lung function.
18. chest percussion vest
Answer
rhythmic percussion of a patient's chest to loosen retained respiratory secretions.
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